OHVIRA syndrome with uterus didelphis in a pediatric patient

Abstract

Herlyn-Werner-Wunderlich syndrome, or obstructed hemivagina and ipsilateral renal anomaly (OHVIRA), is an infrequent Mullerian duct anomaly.  Uterus didelphys, ipsilateral renal agenesis, and unilateral obstructed hemivagina are observed in this anomaly. Usually, symptoms are pelvic pain and mass. But if the patient has not been diagnosed in the early years, infertility could be the first sign. Being able to make diagnoses for these patients, clinicians should have enough information about this syndrome. A 12-year-old virgin patient presented with a urinary tract infection and was diagnosed as a case of OHVIRA syndrome with uterine didelphys. Urinary tract infection has been rarely reported as the first clinical manifestation of this syndrome. She was cured with hemivaginal septal resection and her hematometra was drained. Ohvira syndrome is an infrequent condition. Because of this when a young patient has pelvic mass and pain with renal anomalies, it is important to keep this disease in mind.